81. Tierärztliche Praxis Heft 1/2000 Translate this page Hund. Ein Fallbericht prune belly syndrome-like prostatic anomalyin a dog, Birgit Lindemeier, Kerstin Kohl, Nicole Kirchhof, 111, http://www.schattauer.de/zs/tpK/2000/2/ihv.asp

Zeitschriften Tierärztliche Praxis Kleintiere Jahrgänge Heft 2 2000 ALLGEMEINES U ntersuchungen zur Pharmakokinetik von Coffein, Theophyllin und Theobromin beim Hund I nvestigations on the pharmacokinetics of caffeine, theophylline and theobromide in the dog B. Loeffler, Katharina Kluge, F. R. Ungemach, M. Kietzmann P lasma- und Urinkonzentrationen von Coffein, Theophyllin und Theobromin nach Applikation von Kaffee, Tee und Schokolade bei Hunden und ihre Dopingrelevanz bei Windhundrennen C oncentrations of caffeine, theophylline and theobromine in plasma and urine of dogs after application of coffee, tea and chocolate and its relevance to doping B. Loeffler, Katharina Kluge, F. R. Ungemach, M. Kietzmann HUND/KATZE F elines malignes Lymphom: Ergebnisse der Chemotherapie und prognostische Faktoren (18 Katzen) F ... eline lymphoma: Treatment results and prognostic factors (18 cats) Marion Link, J. Hirschberger K ongenitale peritoneoperikardiale Hernie und Perikardzyste bei einem Hund P eritoneopericardial hernia and pericardial cyst in a dog Inga Stephan, Andrea Meyer-Lindenberg, Marion Hewicker-Trautwein

82. Virtual Children's Hospital: Paediapaedia: Prune-Belly Syndrome (Eagle-Barrett S Paediapaedia Genitourinary Diseases prunebelly syndrome (Eagle-Barrett syndrome).Michael P. D'Alessandro, MD Peer Review Status Internally Peer Reviewed http://www.vh.org/pediatric/provider/radiology/PAP/GUDiseases/Prune.html

Paediapaedia: Genitourinary Diseases Prune-Belly Syndrome (Eagle-Barrett Syndrome) Michael P. D'Alessandro, M.D. Peer Review Status: Internally Peer Reviewed Clinical Presentation: Triad of deficient or absent abdominal musculature, undescended testicles, and dysplasia of the urinary tract. Physical exam shows a wrinkled anterior abdominal wall. Etiology/Pathophysiology: Etiology is unknown.Twenty percent are still born or die as neonates, and an additional 50% die in the first 2 years of life. Other associated anomalies include hip dislocations / club foot / limb deformities (40% ), cardiac defects(30% ), and malrotation (30% ). Pathology: Aplasia of the muscles of the lower medial abdominal wall. The kidneys have a decreased number of functioning nephrons with variable cystic dysplasia. The dilated ureters and bladder have a patchy absence of smooth muscle. Imaging Findings: The ureters and bladder are dilated. Urethral abnormalities that can be seen include posterior urethral dilation, diverticula, stenosis / atresia, and megaurethra. They can have umbilical-bladder attachment or a patent urachus. DDX: Posterior urethral valves References: See References Chapter.

83. Keyword:Eagle-Barrett (prune Belly) Syndrome EagleBarrett (prune belly) syndrome. Chapter 17 The Eagle-Barrettsyndrome is a relatively rare condition in which there is failure http://www.kumc.edu/instruction/medicine/pathology/ed/keywords/kw_eagle-ba.html

Eagle-Barrett (prune belly) syndrome Chapter: 17 The Eagle-Barrett syndrome is a relatively rare condition in which there is failure of normal development of the abdominal muscles and the smooth muscle of the ureters and bladder. Bilateral cryp torch idism is the rule. At times, talipes equinovarus and hip dislocation are also noted. Because the smooth muscle of the ureterotrigonal complex is deficient, reflux is to be expected; advanced hydroureteronephrosis is present.

84. Prune-Belly Syndrome - Page 128 prunebelly syndrome. Pathohistologic examination revealed congenital cysticadenomatoid malformation, type II, as part of prune-belly syndrome. http://www.rbrs.org/database/82-3/page128.html

PRUNE-BELLY SYNDROME M. Van Leersum, C.K. van der Ent, R. Lapham and F.J.A. Beek Key-word: Lung, abnormalities. Clinical history A female neonate, born to a healthy mother (gestational age 39 weeks 1 day) with birth weight of 2280 grams is presented. The Apgar score 5 minutes after spontaneous delivery was 10. Physical examination showed an extremely flabby abdominal wall, with the contour of the intestines standing out through the abdominal wall. On ultrasonography, absence of abdominal musculature was found. The intra-abdominal organs were normal. Chest radiographs and contrastenhanced CT-scan of the thorax were performed. Radiological diagnosis Chest radiograph (AP view) (fig. 1) shows hyperlucency and expansion of the lower lobe of the right lung, displacement of the heart and mediastinum to the left due to increased volume of the right hemithorax. Contrast-enhanced CT scan of the thorax - section at the level of the lower lobe (fig. 2) - demonstrates multiple, medium-sized lucent cystic lesions in the right lower lobe. Mediastinal shift to the left and compression of a normal left lung are noted. The diseased right lower lobe was completely removed surgically. Pathohistologic examination revealed

85. PRUNE-BELLY SYNDROME - M. Van Leersum, C.K. Van Der Ent, R. Lapham And F.J.A. Be . prunebelly syndrome. Pathohistologic examination revealed congenital cysticadenomatoid malformation, type II, as part of prune-belly syndrome. http://www.rbrs.org/journal/volume82/prune_belly.htm

PRUNE-BELLY SYNDROME M. Van Leersum, C.K. van der Ent, R. Lapham and F.J.A. Beek Key-word: Lung, abnormalities Clinical history A female neonate, born to a healthy mother (gestational age 39 weeks 1 day) with birth weight of 2282 grams is presented. The Apgar score 5 minutes after spontaneous delivery was 10. Physical examination showed an extremely flabby abdominal wall, with the contour of the intestines standing out through the abdominal wall. On ultrasonography, absence of abdominal musculature was found. The intra-abdominal organs were normal. Chest radiographs and contrast-enhanced CT-scan of the thorax were performed. Radiological diagnosis Chest radiograph (AP view) (fig. 1) shows hyperlucency and expansion of the lower lobe of the right lung, displacement of the heart and mediastinum to the left due to increased volume of the right hemithorax. Contrast-enhanced CT scan of the thorax - section at the level of the lower lobe (fig. 2)

86. ORPHANET® : 'Prune Belly' Syndrome ORPHANET. ORPHANET database access. 'prune belly' syndrome. Directaccess to details Alias Urethral obstruction sequence. Home Page. http://www.orpha.net/static/GB/prune_belly.html

ORPHANET database access 'Prune belly' syndrome Direct access to details Alias : Home Page

87. Prune Belly (Eagle-Barrett) Syndrome prune belly (EagleBarrett) syndrome. absent abdominal musculature; undescendedtestes; dilated ureters calyces; clubbed feet; heart lung abnormalities. http://chorus.rad.mcw.edu/doc/00336.html

CHORUS Collaborative Hypertext of Radiology GU - Other Feedback Search prune belly (Eagle-Barrett) syndrome absent abdominal musculature undescended testes clubbed feet ** predominantly in males Charles E. Kahn, Jr., MD - 2 February 1995 Last updated 14 March 2001 Medical College of Wisconsin

88. Nature Publishing Group Special Imaging Casebook prunebelly syndrome With Urachal DiverticularCalcification, Posterior Urethral Valves, and Patent Utricle. http://www.nature.com/cgi-taf/DynaPage.taf?file=/jp/journal/v19/n8/abs/7200094a.

89. The Lethal Variant Of The Prune Belly’s Syndrome. Two Cases Report http://www.medigraphic.com/ingles/i-htms/i-h-gral/i-hg1999/i-hg99-3/im-hg993j.ht

90. Abdominal Wall Defect Of The Stomach Abdominal Wall Defects (Congenital). Etiology • Abdominal wall defects includeomphalocele, gastroschisis, limbbody wall complex and prune-belly syndrome. http://radiology.uchc.edu/eAtlas/GI/743.htm

91. Prune Belly-oireyhtymä, Keuhkovaltiomon Ahtauma, Kehitysvammaisuus Ja Kuurous Kehitysvammahuollon tietopankki. Puuttuvat vatsalihakset ja kehitysvammaisuus.prune bellyoireyhtymä, keuhkovaltiomon ahtauma, kehitysvammaisuus ja kuurous. http://www.saunalahti.fi/kup/syndroma/luumu_kv.htm

Kehitysvammahuollon tietopankki Puuttuvat vatsalihakset ja kehitysvammaisuus Prune Belly-oireyhtymä, keuhkovaltiomon ahtauma, kehitysvammaisuus ja kuurous Prune Belly-oireyhtymä, keuhkovaltiomon ahtauma, kehitysvammaisuus ja kuurous on erittäin harvinainen oireisto. Prune Belly-oireyhtymän lisäksi sen keskeisiä piirteitä ovat aistinhermojen vaurioitumisesta kuurous ja vaihtelevan tasoinen kehitysvammaisuus sekä keuhkovaltimon synnynnäinen ahtauma. Vammautuminen on lievempää tytöillä kuin pojilla. Sairaus on joko autosomaalisesti peittyvästi tai X-kromosomin kautta periytyvä Lisätietoja: BRUNE BELLY SYNDROME, WITH PULMONIC STENOSIS, MENTAL RETARDATION, AND DEAFNESS, OMIM ABDOMINAL MUSCLES, ABSENCE OF, WITH URINARY TRACT ABNORMALITYS AND CRYPTORCHIDISM, OMIM Prune Belly Syndrome, NORD The Prune Belly Syndrome Network Kari Viitapohja 30.3.2000 Kehitysvammaisten Uudenmaan tukipiiri ry. Kehitysvammahuollon tietopankki

92. Prune Belly-oireyhtymä Kehitysvammahuollon tietopankki. Puuttuvat vatsalihakset, virtsateidenpoikkeavuudet ja piilokivekset. prune bellyoireyhtymä. prune http://www.saunalahti.fi/kup/syndroma/luumumah.htm

Kehitysvammahuollon tietopankki Puuttuvat vatsalihakset, virtsateiden poikkeavuudet ja piilokivekset Prune Belly-oireyhtymä Prune Belly-oireyhtymä (prune = kuivattu luumu, belly = vatsa), joka tunnetaan myös Eagle-Barretin syndroomana, on harvinainen sairaus. Sille on luonteenomaista vatsalihasten osittain tai kokonaan puuttuminen, piilokiveksisyys ja virtsateiden epämuodostumat. Virtsanjohtimet ovat laajentuneet, samoin munuaisallas. Virtsan takaisinvirtaus johtimista rakkoon on tavallista. Lisäksi oireyhtymään voi liittyä keuhkojen kehittymättömyyttä. Synnynnäinen oireisto, jonka syytä ei tiedetä, on yleisempi poika- kuin tyttövauvoilla. Lisätietoja: ABDOMINAL MUSCLES, ABSENCE OF, WITH URINARY TRACT ABNORMALITYS AND CRYPTORCHIDISM, OMIM Prune Belly Syndrome, NORD The Prune Belly Syndrome Network Prune Belly-oireyhtymä, keuhkovaltiomon ahtauma, kehitysvammaisuus ja kuurous, Kehitysvammahuollon tietopankki Kari Viitapohja 30.3.2000 Kehitysvammaisten Uudenmaan tukipiiri ry. Kehitysvammahuollon tietopankki

93. Lancaster General - Genitourinary And Kidney Disorders 300,000 children will develop disorders that cause blood and protein to leak intotheir urine, such as hemolytic uremic syndrome and glomerulonephritis. http://www.lha.org/content/greystone_6995.asp

94. Pakistani Medical And Health Portal HYTRIN You have a choice that's right for your patients Urology PruneBelly syndrome and Tracheoesophageal Fistula in a Premature Neonate. http://www.pakdoctor.com/health_professional/urology/Prune_Belly.html

News Health Professionals General Public Students ... HYTRIN You have a choice that's right for your patients... Urology Prune Belly Syndrome and Tracheo-esophageal Fistula in a Premature Neonate Prune Belly Syndrome, also known as Eagle-Barrett syndrome, is awell known triad of abdominal muscle deficiency or hypoplasia, urinarytract anomalies, and bilateral cryptorchidism.1 Tracheo-esophagealfistula is a sporadically occurring defect estimated to occur in 1 out4425 live births.2 Only one case of Prune Belly Syndrome, tracheo-esophagealfistula associated with VATER syndrome, and urethral atresia occurringin the same individual has been reported.3 We present a uniquecase involving a 33 week fetus with bladder distention and bilateral hydroureteronephrosisdiagnosed in utero who postnatally was diagnosed with Prune Belly Syndrome,tracheo-esophageal fistula, and urethral atresia. CASE REPORT DISCUSSION The Prune Belly Syndrome in females is a rarer occurrence than in maleswith an observed prevalence in males of 5/100,000 versus 1/100,000 in females.By definition this syndrome is only completely expressed in males(presenceof cryptorchidism mandatory), however, three percent of the reported casesoccur in genetic females and is generally known as Pseudo-Prune Belly Syndrome(PPBS).4,5 Our patient was found to have the typical phenotypeof PPBS, lax abdominal musculature, large distended bladder, and urethralatresia as well as an unilateral absent ovarian structure, absent leftfallopian tube and atretic vagina. These anomalies are consistent withother reported cases of PPBS in which vaginal atresia, bicornuate uterus,urethral atresia, and hydronephrosis are commonly noted.6

A  B  C  D  E  F  G  H  I  J  K  L  M  N  O  P  Q  R  S  T  U  V  W  X  Y  Z

Page 5     81-94 of 94    Back | 1  | 2  | 3  | 4  | 5