Extractions: (advertisement) Home Specialties CME PDA ... Patient Education Articles Images CME Patient Education Advanced Search Link to this site Back to: eMedicine Specialties Medicine, Ob/Gyn, Psychiatry, and Surgery Gastroenterology Last Updated: February 15, 2002 Rate this Article Email to a Colleague Synonyms and related keywords: MAP, Kohlmeier-Degos syndrome, Degos disease, vascular occlusive disorders, thromboangiitis obliterans AUTHOR INFORMATION Section 1 of 10 Author Information Introduction Clinical Differentials ... Bibliography Author: Hemant Pande, MD , Former Fellow, Department of Gastroenterology, Johns Hopkins Bayview Medical Center Coauthor(s): Lawrence Cheskin, MD , Chief, Associate Professor, Department of Medicine, Division of Gastroenterology, Bayview Medical Center, Johns Hopkins University School of Medicine Brian Lacy, MD , Medical Director of Motility Center, Assistant Professor, Department of Internal Medicine, Division of Gastroenterology, Bayview Medical Center, Johns Hopkins University
Degos Disease - 1 Degos' Disease malignant atrophic papulosis. Return to Image Index page. http://tray.dermatology.uiowa.edu/Degos01.htm
Arch Dermatol -- Page Not Found DIAGNOSIS malignant atrophic papulosis (Degos disease). HISTOPATHOLOGIC FINDINGSThe epidermis appears thin. 3. Degos R. malignant atrophic papulosis. http://archderm.ama-assn.org/issues/v134n2/ffull/dof0298-4b.html
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Extractions: Requena L; Farina C; Barat A; Department of Dermatology, Fundacion Jimenez Diaz, Universidad; Autonoma, Madrid, Spain. Abstract: Malignant atrophic papulosis is a rare disorder characterized by pathognomonic cutaneous lesions that consist of infarctive thrombosis. Visceral involvement often occurs; the gastrointestinal tract and the central nervous system are most frequently involved. Malignant atrophic papulosis has not been previously described in an AIDS patient. We describe a 58-year-old homosexual man with AIDS who developed typical cutaneous lesions of malignant atrophic papulosis. No visceral involvement has been detected in 2 years. Keywords: *Acquired Immunodeficiency Syndrome/COMPLICATIONS *Skin Diseases, Papulosquamous/COMPLICATIONS *Skin Diseases, Vascular/COMPLICATIONS
Malignant Atrophic Papulosis - General Practice Notebook Notebook. malignant atrophic papulosis. Dego's disease is a rare, lethalcondition affecting the skin, gut and nervous system. Presentation http://www.gpnotebook.co.uk/cache/60424212.htm
EMedicine - Malignant Atrophic Papulosis : Article Excerpt By: Hemant Pande, MD malignant atrophic papulosis Kohlmeier described a case of malignant atrophic papulosis (MAP) as a form of thromboangiitis obliterans in 1941. It was recognized as a distinct clinical entity by Degos in 1942, hence the name. Excerpt from malignant atrophic papulosis. Synonyms, Key Words, and Related Terms MAP, Kohlmeier-Degos syndrome, Degos http://www.emedicine.com/med/byname/malignant-atrophic-papulosis.htm
Extractions: (advertisement) Synonyms, Key Words, and Related Terms: MAP, Kohlmeier-Degos syndrome, Degos disease, vascular occlusive disorders, thromboangiitis obliterans Background: Kohlmeier described a case of malignant atrophic papulosis (MAP) as a form of thromboangiitis obliterans in 1941. It was recognized as a distinct clinical entity by Degos in 1942, hence the name. Pathophysiology: MAP is a multisystem disorder involving the small-caliber blood vessels. The disease is characterized by narrowing and occlusion of the lumen by intimal proliferation and thrombosis, which leads to ischemia and infarction in the involved organ systems. MAP is different from other vasculitides in that inflammation is not a prominent component of the disease. MAP may involve the gastrointestinal and genitourinary tracts, central and peripheral nervous systems, skin, heart, lungs, eyes, pancreas, adrenals, and kidneys. The disease involves the skin alone in 37% of cases. The gastrointestinal tract is involved in about 50% of cases. Frequency:
Www.GPnotebook.co.uk (letter M , Terms 81 To 100) male puberty male sterilisation malformation (congenital) Malgaigne's luxationmaligant disease in childhood malignant atrophic papulosis malignant central http://www.gpnotebook.co.uk/list.cfm?ID=m&start=81
Degos Disease An in depth look at degos disease including prognosis and treatment.Category Health Conditions and Diseases Rare Disorders Degos The skin biopsy places the pathologist at the center of the diagnostic evaluation.SYNONYMS, malignant atrophic papulosis KöhlmeierDegos' disease. http://www.thedoctorsdoctor.com/diseases/degos_disease.htm
Extractions: Background This rare disease is important because a skin biopsy may be the first clue to the diagnosis. Patients classically develop multiple skin papules that evolve to have a dimpled appearance with a porcelain white center. This is the clue to the underlying disease which can affect the gastrointestinal tract and central nervous system and may lead to death. The skin biopsy places the pathologist at the center of the diagnostic evaluation. SYNONYMS Malignant Atrophic Papulosis Köhlmeier-Degos' disease INCIDENCE Rare DISEASE ASSOCIATIONS CHARACTERIZATION Familial cases Rare PATHOGENESIS CHARACTERIZATION Unknown-has been considered a vasculitis, mucinosis, or thrombotic disorder No circulating immune complexes, anti-endothelial cell antibodies, or anticardiolipin antibodies identified Endovasculitis Some consider a primary endothelial cell defect with secondary thrombosis leading to infarctive changes LABORATORY/RADIOLOGIC/OTHER TESTS CHARACTERIZATION Impaired fibrinolytic activity Alterations in platelet function GROSS APPEARANCE/CLINICAL VARIANTS CHARACTERIZATION Classic Skin Lesions Crops of papules ranging from 0.5-1 cm which develop an umbilication with a porcelain white center with a telangiectatic ring
Extractions: Degos disease in a 24-year-old Jordanian male R.M. Al-Smadi, F. Abu-Jamous and I. Omeish Volume 6, Issue 1, 2000, Page 194-196 Introduction Degos disease (malignant atrophic papulosis) is a rare disease that affects skin and the gastrointestinal, ocular and central nervous systems. The disease is characterized by papules that develop porcelain-white centres and telangiectatic borders. The etiology of the disease is unknown; however, the immediate cause may lie in impaired endothelial function or abnormal coagulation (fibrinolytic activity). Viral causes have been implicated. Histopathological findings are wedge-shaped areas of dermal necrosis covered by markedly atrophic malpighian layers and collagen with a smudged appearance. Complications of the disease include peritonitis, intestinal perforation and, less frequently, cerebral infarction. There is no effective treatment; however, antiplatelet therapy may be beneficial for patients in whom platelet aggregation is impaired. Prognosis is poor when systemic involvement is found, but seems to be good in benign forms.
PaperChase Search Page (custom) Degos' disease (malignant atrophic papulosis) is a rare multisystemic disease with characteristic cutaneous lesions, http://www.paperchase.com/docs/R1603/F205201/B8.htm
Extractions: A 31-year-old woman presented with symptoms and signs of constrictive pericarditis. She had a history of Degos' disease, a rare disorder characterized by skin and bowel lesions thought to be secondary to vasculitis. A chest roentgenogram showed Top of Abstract extensive calcification of the pericardium. Although pleural and pericardial involvement has been reported in this disease, constrictive pericarditis is most unusual, and radiographically demonstrable calcification of the pericardium has not been reported previously. Degos' disease (malignant atrophic papulosis) is a rare multisystemic disease with characteristic cutaneous lesions, abdominal symptoms and often rapidly fatal course. Our review of the reported intrathoracic involvement in the more than 60 reported cases of Degos' disease suggests that pleuritis and pericarditis are manifestations of the
Health Library - Degos Disease Synonyms. Degos Syndrome; DegosKohlmeier Disease; Kohlmeier-Degos Disease;malignant atrophic papulosis. Disorder Subdivisions. None. General Discussion. http://health_info.nmh.org/Library/HealthGuide/IllnessConditions/topic.asp?hwid=
Springer LINK Der Hautarzt - Abstract Volume 53 Issue 1 (2002) Translate this page malignant atrophic papulosis not always malignant! C. Mensing, H. Mensing. A patientdeveloped malignant atrophic papulosis with only cutaneous manifestation. http://link.springer-ny.com/link/service/journals/00105/bibs/2053001/20530042.ht
PaperChase Search Page (custom) 90269270 (Reference 46 of 210) Flag for Printing. An atypical paediatriccase of malignant atrophic papulosis (KohlmeierDegos disease). http://www.paperchase.com/docs/R1603/F205201/B16.htm
Extractions: A new case of malignant atrophic papulosis (Kohlmeier-Degos disease) is reported. Vascular symptoms began at 17 months of age with cerebral ischaemia and progressive involvement of fingers and toes with torpid ulcers and apical necrotic amputations. At 6 years of age he developed chronic intestinal ischaemia with malabsorption and a new cerebral attack; in spite of Top of Abstract anti-aggregant therapy the disease progressed and he died 7 months after diagnosis from a third cerebral ictus. Since the typical skin lesions of the disease were absent, the diagnosis was made on the basis of a pathological pattern of an occluded biopsied artery. The elder brother presents clinical and instrumental vascular involvement without cutaneous lesions and could be slightly affected.
Dorlands Medical Dictionary malignant atrophic papulosis, an often fatal disease occurring most often in men,characterized by endovasculitis of the skin, gastrointestinal tract, and http://www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspzQzpgzEzzSzppdocszSzuszS
