Uhrad.com Pediatric Imaging Teaching Files Discussion Enchondromatosis (ollier's disease) is a non hereditary disorder of enchondral ossification with lesions http://www.uhrad.com/pedsarc/peds055.htm
Extractions: Click on Images for Enlarged View Clinical History: Trauma to second right digit. Findings: Multiple lucent metaphyseal lesions of the proximal and middle phalanges of the fourth and fifth digits, as well as the distal metacarpals of the fourth and fifth digits. Diagnosis: Multiple enchondromatosis. Discussion: Enchondromatosis (Ollier's Disease) is a non hereditary disorder of enchondral ossification with lesions distributed throughout the tubular and flat bones of the body. The presenting clinical manifestations are masses that increase in size as the child grows, asymmetric limb shortening and either genu varus or genu valgus deformities. Radiographs of the young child could be normal in the first few years of life and later demonstrate radiolucent streaking within the metaphysis of involved bones, or at infancy may demonstrate radiolucent masses which can be round, triangular or linear. Stippled calcifications occur with age within the enchondromas. There may be considerable expansion of the tubular bones especially in the hands, and pathologic fractures may occur. Cartilaginous areas extending from the physis can lead to a growth interference resulting in limb shortening and deformities. Enchondromas typically stabilize or regress in adulthood. However, sarcomatous transformation has been described. Six types of enchondromatosis have been described, of which three are more common. If the multiple enchondromas are purely unilateral or unevenly distributed throughout the metaphyses of the long bones, sparing the cranium and spine, it is called Ollier's Disease. If the enchondromas are seen with multiple cutaneous hemangiomas (soft tissue calcifications/phleboliths) it is called Maffucci's Syndrome. If there is symmetric involvement throughout the body including the cranium, hands and feet, it is known as generalized enchondromatosis. The Ollier's and Maffucci's are more common in boys (2:1). The less frequent types include metachondromatosis which affects the short tubular bones of the hands and feet, and spondyloenchondroplasia in which the enchondromas are associated with platyspondyly, and enchondromas with irregular vertebral bodies.
The Contact A Family Directory - OLLIER'S DISEASE printer friendly, ollier'S disease, ollier'S disease SELFHELP GROUP.Andrew Harter ollier's disease Self-Help Group Tithings New Barn http://www.cafamily.org.uk/Direct/o12.html
Extractions: printer friendly OLLIER'S DISEASE home more about us in your area conditions information ... how you can help search this site Ollier's Disease: Enchondromatosis An Enchondroma is an island of unossified hyaline cartilage situated within bone (cartilage is the precursor of bone). They are usually multiple, affecting one or several bones. Characteristically, it is an asymmetric disorder, confined to one side of the body. The bones most commonly affected are the long bones, pelvis and bones of the hand. The islands of cartilage appear early in childhood and can develop, but it is very unusual for additional lesions to appear after puberty. Ollier's Disease is a very rare disorder which affects both sexes. It presents either as a lump or swelling or deformity of the long bone in early childhood. As the bones are weakened, they may fracture but healing is normal. The severity varies but otherwise the child develops normally. The main complications are the nature of the lump or swelling, the deformity of the affected bone and the shortening of the affected bone. The deformity can be corrected by osteotomy and the shortening can be addressed by leg lengthening in the knowledge that the bones will heal normally. Differential diagnoses of fibrous dysplasia and diaphyseal aclasis need to be considered. There is practically no likelihood of malignancy. Maffucci Syndrome in which there are cutaneous haemangionates associated with the enchondromas does carry a definite risk of malignancy. However, this is a separate and even rarer condition.
Foot Problems > Diseases Of The Foot > Ollier's Disease diseases of the foot ollier's disease. ollier's disease is usually associated with a bony prominence under the toenail. http://www.thefootspecialists.com/prob_diseases_ollier.php
The Family Village / Library / Ollier's Disease Library O P. ollier's disease. Related Disorders plans. OSFHG publishesthe ollier's disease Self-Help Group Newsletter, quarterly. They http://www.familyvillage.wisc.edu/lib_olli.htm
Extractions: Web: http://uhsweb.edu/olliers/olliers.htm Mission - to establish means of communication for those burdened with the disease, and to inform the world at large about those people's plight. Additionally, they wish to help people with the disease cope with its physical and psychological burden, provide a forum to discuss Ollier problems or help others to cope with theirs, collect data on research conducted on the disease and/or in related fields, and raise awareness of our existence, activities and plans. OSFHG publishes the Ollier's Disease Self-Help Group Newsletter, quarterly. They have developed a pamphlet that provides information on the disease and the organization. They provide a new parent packet, please send a stamped self-addressed envelope. The Group has a bibliography of articles on the disease that is available to members upon request. The Group collects information on physicians and researchers who treat/study the condition and disseminates this information through the newsletter.
Health Library - Ollier's Disease ollier's disease. Founded 1985.Mutual support and exchange of ideas for personswith ollier's or Maffucci's disease, their families and physicians. http://yalenewhavenhealth.org/Library/HealthGuide/SelfHelp/topic.asp?hwid=shc29o
Health Library - Ollier's Disease ollier's disease. Founded 1985.Mutual support and exchange of ideas for personswith ollier's or Maffucci's disease, their families and physicians. http://www.laurushealth.com/library/healthguide/selfhelp/topic.asp?hwid=shc29oll
Birth Disorder Information Directory - O Lethal Type See Young McKeever Squier Syndrome. ollier's disease (Dyschondroplasia,Multiple Enchodromatosis, Osteochondromatosis) http://www.bdid.com/defecto.htm
Extractions: A disorder of the growing ends of bones in which round nonossified cartilaginous masses scattered throughout the skeleton produce asymmetrical and very variable deformities, asymmetric leg shortening being common. The lesions are first noted from 1 to 4 years of age, rarely at birth, with little progression after adolescence. Both sexes may be affected. The majority of cases have been sporadic but a familial tendency has been reported in a few instances. Enchondromatosis is usually bilateral. The term Ollier syndrome applies in cases with unilateral involvement. The combination of multiple enchondromata with haemangiomata and phleboliths is known as Maffucci syndrome.
Louis Xavier Édouard Léopold Ollier (www.whonamedit.com) Associated with KlippelTrénaunay-Weber syndrome,ollier's disease,ollier'slayer,ollier-Thiersch graft. Who named it? olliers disease. http://www.whonamedit.com/doctor.cfm/477.html
Extractions: Louis Xavier Édouard Léopold Ollier is particularly remembered for his work on bone and joint surgery. He was born in Vans, Ardèche, where both his father and his grandfather had been doctors. He initially studied natural science at Montpellier and in 1849 was assistant in botany in the faculty of medicine.
Extractions: Dyschondroplasia: Ollier's Disease and Maffucci's Disease This page is for informational purposes only. I have placed it here as a public service. I believe it is accurate, but I cannot accept liability for the contents of this page. A visitor would be very foolish to trust information from a single source, or to consider any reading a substitute for a personal physician. Please send your suggestions and corrections to erf@alum.uhs.edu What is Ollier's disease? An enchondroma is a bit of cartilage (gristle) that has been left behind during the early development of a bone. As the bone lengthens, it gets dragged toward the shaft of a bone, where it begins growing on its own. They are probably not true tumors. The commonest site for enchondromas is the hands, followed by the feet and forearms. The skull, spine, and breastbone are seldom affected. What problems result from enchondromas?
Ollier's Disease ollier's disease. Definition ollier's disease is a condition that ischaracterized by multimple enchondromas throughout the skeleton. http://orthopedics.about.com/library/glossary/bldef-olliers.htm
Extractions: Definition: Ollier's Disease is a condition that is characterized by multimple enchondromas throughout the skeleton. Patient's with Ollier's Disease will regularly see the orthopedist for monitoring of their symptoms. Approximately 30% of patients with Ollier's disease will develop malignancies of their tumors. It is important to recognize these changes in order for prompt treatment of the lesion. Related Resources: Bone Tumors
Enchondroma There is a syndrome called ollier's disease in which patients havemany enchondromas. These must be carefully monitored as there http://orthopedics.about.com/library/glossary/bldef-enchondroma.htm
Extractions: Definition: An enchondroma is a benign tumor of cartilage. This type of tumor causes the formation of islands of mature cartilage in abnormal locations. Usually these tumors occur in the hands or in the long bones of the arms and legs. They are most often asymptomatic, and do not cause pain. If you do experience symptoms, these tumors can be removed; however, this is a risk of recurrence following surgery. There is a syndrome called Ollier's Disease in which patients have many enchondromas. These must be carefully monitored as there is about a 30% risk of these patients developing a malignant form of the enchondroma called chondrosarcoma. Another familial disorder of multiple enchondromas is called Mafucci syndrome. In this disease there is almost a 100% certainty of the development of malignant tumors. Related Resources: Bone Tumors
Ollier Translate this page ollier's disease ist eine sehr seltene Krankheit, bei der sich Tumore in den langenArm- und Bein-knochen bilden und das normale Knochen-Wachstum hindern. http://www.ollier-maffucci.org/german_group.htm
Extractions: The Ollier/Maffucci Self-Help Group French German Spanish ... Inspirations Ollier/Maffucci Selbst-Hilfe Gruppe Inhalt Unsere Mission, Ziele und kurzfristigen Aufgaben Was ist Ollier's oder Maffucci's Disease? * Online Newsletters in Englisch * Wie erreicht man die Ollier/Maffucci Selbsthilfe Gruppe? ... Unsere Mission ist Kommunikationsmöglichkeiten für unsere Mitglieder zu schaffen und die Welt über die Krankheit und Probleme der Patienten zu informieren Unsere Ziele sind: Unsere kurzfristigen Aufgaben sind Anfang Disease Englisch Kontakte ... Home Was ist Ollier's oder Maffucci's Disease?
Bilateral Presentation Of The Ollier's Disease.... Bilateral presentation of the ollier's disease A case report, and literature review.ABSTRACT. Key words Enchondromas, osteochondromas, ollier´s disease. http://www.imbiomed.com.mx/HG/Hgv64n3/english/Zhg013-05.html
Extractions: ABSTRACT Among the cartilaginous tumors, the enchondromas and osteochondromas are benign lesions formed by mature hyaline cartilage that affect the tubular bones of the hand and most commonly, the middle and proximal phalanges, and can be multiple o single lesions. When the enchondromas appear in the early childhood, are multiple lesions with no specific hereditary pattern, are known as Ollier's disease. Another feature of this disease is the unilateral appearance, affecting mainly hands and feet. In this article we present the case of a 18 years old male, with diagnosis of Ollier's disease since he was 2 years old, with affection of both hands and feet, most severely affected in the right upper extremity. The patient was treated with functional aesthetic amputation of 4 th and 5 th fingers and tumor resection of 2 nd and 3 rd fingers of his right hand. There are very few cases reported in the literature with such a severe deformity of the hand, and in spite of what have been described previously, in this case, the disease has not been self limited, to the contrary, it has recurred even more aggressively each time, now affecting the four extremities, thus raising the chance of malignant transformation, which makes indispensable to have a close follow up of the patient for a long time.
Wheeless' Textbook Of Orthopaedics Main Menu Home Page Multiple Enchodromatosis (ollier's disease). Discussion Themalignant potential of enchondromatosis ollier's disease. An http://www.ortho-u.net/o6/93.htm
Extractions: Main Menu Home Page - Discussion: - originally was described by Ollier in late 1800's; - characterized by multiple enchondroma lesions primarily located w/ in the metaphyseal regions of tubular bones; - usually diagnosed in childhood; - pts w/ Ollier's dz have increased risk of a secondary chondrosarcoma developing later in life; - risk is about 25% by age 40 yrs; - Clinical Findings: - most pts have bilateral involvement, w/ predominance on one side; - enchondromas most frequently involve the short tubular bones of hands - Radiographs: - in most cases, there will be diaphyseal lesions or metaphyseal lesions which do not cross the growth plate, at least, not until growth plate closure; - in some cases enchondromatosis will affect patients in the metaphyseal and epiphyseal regions; - when enchondromas cross the growth plate, severe limb length deformities and angular deformities will develop; The malignant potential of enchondromatosis Ollier's Disease. An assessment of angular deformity, shortening, and
Wheeless' Textbook Of Orthopaedics Main Menu Home Page ollier's disease. An assessment of angular deformity, shortening,and. A retrospective review of twentyone patients with ollier's disease. http://www.ortho-u.net/l8/205.htm
Extractions: Main Menu Home Page pathological fracture in twenty-one patients. Shapiro-F J-Bone-Joint-Surg-Am. 1982 Jan; 64(1): 95-103 A retrospective review of twenty-one patients with Ollier's disease showed that the lesion involved the femur and tibia most frequently, and that those bones accounted for the large majority of clinical problems. Angular deformities were common; 80 per cent of the affected femora had clinically significant varus or valgus angulation in the distal part and 42 per cent of the affected tibiae had proximal or distal deformity. The apex of the angulation, when present, was metaphyseal, with the concavity on the side that was more extensively involved by the enchondromas. Osteotomies were done frequently to correct angulation; all healed well. Deformity in the distal part of the femur frequently required repeat osteotomy to achieve a straight bone at skeletal maturity, The extent of shortening, which always was present in the involved limb, closely
Health Library - Ollier's Disease Search. ollier's disease. Founded 1985.Mutual support and exchange of ideas forpersons with ollier's or Maffucci's disease, their families and physicians. http://yourhealth.stlukesonline.org/Library/HealthGuide/SelfHelp/topic.asp?hwid=
