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Porphyrias: more books (87)

PORPHYRIA CUTANEA TARDA Don't forget to look at the urine by Michael W. Rich MD, 2010-06-20

Acute Intermittent Porphyria

Porphyria and King George III by Ida Macalpine, 1969

Porphyria -- A Royal Malady by Ida Wertheimer Macalpine, 1968

Porphyria -- A Royal Malady by Ida [Wertheimer] [Macalpine, 1968-01-01

Porphyrias: Porphyria, Porphyria Cutanea Tarda, Erythropoietic Protoporphyria, Acute Intermittent Porphyria, Variegate Porphyria

Porphyria Cutanea Tarda. New Facts on Aetiology, Pathogenesis, Clinical Manifestations and Treatment. by Lubor, Jaromir Chlumsky and Alena Chlumska Malina, 1974

Robert Browning's "Porphyria's Lover": A Study Guide from Gale's "Poetry for Students" (Volume 15, Chapter 11)

Porphyria - A Bibliography and Dictionary for Physicians, Patients, and Genome Researchers by Philip M. Parker, 2007-07-18

Porphyrias: An entry from Gale's <i>Gale Encyclopedia of Medicine, 3rd ed.</i> by Julia Barrett, Judy, MS Hawkins, et all 2006

21st Century Ultimate Medical Guide to Porphyria - Authoritative Clinical Information for Physicians and Patients (Two CD-ROM Set) by PM Medical Health News, 2009-06-06

Gale Encyclopedia of Medicine: Porphyrias by Judy C. Hawkins MS, 2002-01-01

Amanita: Amanita virosa, Amanita verna, Amanita phalloides, Amanita citrina, Amanita gemmata, Amanita porphyria, Amanita fulva, Amanita regalis (German Edition)

Porphyrias Edition by Geoffrey Dean, 1971-01-01

lists with details

Romance & Love For Single Men And Single Women
Romance Love For Single Men and Single Women find your match inthis biggest online collection of romance ads. Romantic Singles
http://personal.classmates.lt/matchmakingservice/porphyrias-lover.htm

Extractions: Romantic Singles, Dating Couples, Lovely Ladies... How to find them? Its all here! Largest selection of quality romantic ads listing BEAUTIFUL WOMEN and MEN from all major cities and around the world! You will meet someone beautiful and special on this online service. Place your ad and photos for free and meet your love or friend. Use chat room or search engine to help yourself find the right person! Site ENTRY herpes dating home sitcom friend up hot japanese girl russian boy love vegetarian lifestyle the way you love me boy love gay lover free love love you aphrodisiac for woman black lover free black woman pic gay male love gay man free photo romantic love web personal white wanting black lover uk photo personal tell someone you you know you re dating love connection the lover ... my little lover
Porphyrias Lover, Romantic Times, Single Black Female
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Porphyria Metabolites Enzymes Glycine + Succinyl CoA 5-ALA
Haem, . Globin. . Apoprotein. Haemoglobin. Respiratory pigments. Acute porphyrias. NonAcute, or Cutaneous porphyrias. Porphyrins deposited in upper epidermis.
http://www.users.dircon.co.uk/~rosebud/anaesthesia/porphyrias.html

Extractions: Glycine + Succinyl CoA 5-ALA Plumboprophyria ALA dehydratase Porphobilinogen PBG in urine Acute Intermittant porphyria PBG deaminase Hydroxymethylbilane Uropphyrinogen I Congenital Porphria Uroporphyrinogen cosythetase Uroporpyrinogen III Porphyria cutanea tarda Uroporpyrinongen decarboxylase Coproporrphyrinogen III Hereditary coprophyria Coproporphyrinogen oxidase Protoporphyrinogen IX Variegate porphyria Protoporhyrinogen oxidase Protoporphyrin IX . Iron (Fe ++) Erythropoeitic porphyria Ferrochelatase Haem . Globin . Apoprotein Haemoglobin Respiratory pigments
Porphyrias | Ahealthyme.com
porphyrias Barrett, Julia. Definition. The porphyrias precursor. Thissituation is the main characteristic of the porphyrias. Owing
http://www.ahealthyme.com/article/gale/100083892

Extractions: The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing nonprotein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes. Excess porphyrins are excreted as waste in the urine and stool. Overproduction and overexcretion of porphyrins causes low, unhealthy levels of heme and certain important enzymes, creating various physical symptoms. Description Biosynthesis of heme is a multistep process that begins with simple molecules and ends with a large, complex heme molecule. Each step of the chemical pathway is directed by its own task-specific protein, called an enzyme. As a heme precursor molecule moves through each step, an enzyme modifies the precursor in some way. If a precursor molecule is not modified, it cannot proceed to the next step, causing a buildup of that specific precursor. This situation is the main characteristic of the porphyrias. Owing to a defect in one of the enzymes of the heme biosynthesis pathway, protoporphyrins or porphyrins (heme precursors) are prevented from proceeding further along the pathway. These precursors accumulate at the stage of the enzyme defect causing an array of physical symptoms in an affected person. Specific symptoms depend on the point at which heme biosynthesis is blocked and which precursors accumulate. In general, the porphyrias primarily affect the skin and the nervous system. Symptoms can be debilitating or life threatening in some cases. Porphyria is most commonly an inherited condition. It can also, however, be acquired after exposure to poisonous substances.
Porphyrias | Ahealthyme.com
You are here Home Health A to Z porphyrias. porphyrias. Barrett, Julia. Theporphyrias. In Williams Hematology, edited by Ernest Beutler, et al.
http://www.ahealthyme.com/topic/topic100587325

Extractions: The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing nonprotein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes. Excess porphyrins are excreted as waste in the urine and stool. Overproduction and overexcretion of porphyrins causes low, unhealthy levels of heme and certain important enzymes, creating various physical symptoms. Description Biosynthesis of heme is a multistep process that begins with simple molecules and ends with a large, complex heme molecule. Each step of the chemical pathway is directed by its own task-specific protein, called an enzyme. As a heme precursor molecule moves through each step, an enzyme modifies the precursor in some way. If a precursor molecule is not modified, it cannot proceed to the next step, causing a buildup of that specific precursor. This situation is the main characteristic of the porphyrias. Owing to a defect in one of the enzymes of the heme biosynthesis pathway, protoporphyrins or porphyrins (heme precursors) are prevented from proceeding further along the pathway. These precursors accumulate at the stage of the enzyme defect causing an array of physical symptoms in an affected person. Specific symptoms depend on the point at which heme biosynthesis is blocked and which precursors accumulate. In general, the porphyrias primarily affect the skin and the nervous system. Symptoms can be debilitating or life threatening in some cases. Porphyria is most commonly an inherited condition. It can also, however, be acquired after exposure to poisonous substances.
Porphyrias
porphyrias. Definition The porphyrias are a group of rare disordersthat affect heme biosynthesis. Heme is an essential
http://www.chclibrary.org/micromed/00061410.html

Extractions: Biosynthesis of heme is a multistep process that starts with simple molecules and ends with a large, complex heme molecule. Each step of the biosynthesis pathway is directed by its own task-specific protein, called an enzyme. As a heme precursor molecule moves through each step, an enzyme modifies it in some way. If the precursor is not modified, it cannot proceed to the next step. This situation is the main characteristic of the porphyrias. Owing to a defect in one of the enzymes of the heme biosynthesis pathway, protoporphyrins or porphyrin (heme precursors) are prevented from proceeding further along the pathway. Instead, precursors accumulate at the stage of the enzyme defect and cause an array of physical symptoms in the affected person. Specific symptoms depend on the point at which heme biosynthesis is blocked and which precursors accumulate. In general, the porphyrias primarily affect the skin and the nervous system. Symptoms can be debilitating or life threatening in some cases. Porphyria is an inherited condition, but it may be acquired after exposure to poisonous substances. Heme
The Porphyrias
The porphyrias by Shane Greene, Pharm.D. Introduction The porphyrias are a groupof inherited or acquired genetic defects in the heme biosynthetic pathway.
http://www.clevelandclinicmeded.com/medical_info/pharmacy/septoct1999/pharm.htm

Extractions: by Shane Greene, Pharm.D. Introduction: The porphyrias are a group of inherited or acquired genetic defects in the heme biosynthetic pathway. These defects cause complete or near complete inactivation of the genes encoding for the enzymes that catalyze the transformation of porphyrin precursors. A deficiency in one of these enzymes leads to overproduction and accumulation of these precursors. The specific type of porphyria depends on the location of the accumulation and the enzyme affected. The porphyrias mainly manifest as effects on the nervous system and skin. Classification: The porphyrias are classified as either hepatic or erythropoietic. Hepatic porphyrias have normal red blood cell porphyrin concentrations and present clinically with neurologic symptoms, abdominal pain, neuropathy, and/or psychiatric symptoms. Erythropoietic porphyrias present with an increased concentration of porphyrin within the red blood cells and cutaneous photosensitivity manifestations. Epidemiology: Etiology and Pathogenesis: A different gene encodes each enzyme within the heme biosynthetic pathway. A deficiency in one of the genes is associated with a specific type of porphyria
CCHS Clinical Digital Library
Disorders. porphyrias Clinical Resources. INFO ) Chapter 346 Theporphyrias Table of contents Heme Biosynthesis Access document;
http://cchs-dl.slis.ua.edu/clinical/metabolism/inborn/porphyria.htm

Extractions: Clinical Resources by Topic: Metabolic Disorders Porphyrias Clinical Resources Emergency Pediatrics Atlases Radiology ... Miscellaneous Resources See also: Acute Intermittent Porphyria: Access document Porphyria Cutanea Tarda: Access document Hereditary Coproporphyria: Access document Variegate Porphyria: Access document The Erythropoietic Porphyrias: Access document Congenital Erythropoietic Porphyria: Access document Erythropoietic Protoporphyria: Access document Hoffman: Hematology: Basic Principles and Practice 3rd Ed.-2000 (MD Consult):
9.8.2 Acute Porphyrias - BNF
9.8.2, Acute porphyrias. The acute porphyrias (acute intermittent porphyria,variegate porphyria, hereditary coproporphyria and 5aminolaevulinic
http://bnf.vhn.net/bnf/documents/bnf.1935.html

Extractions: Treatment of serious or life-threatening conditions should not be withheld from patients with acute porphyria. Where there is no safe alternative, urinary porphobilinogen excretion should be measured regularly; if it increases or symptoms occur, the drug can be withdrawn and the acute attack treated.
Drugs Unsafe For Use In Acute Porphyrias - BNF
Drugs unsafe for use in acute porphyrias The following list contains drugs on theUK market that have been classified as unsafe in porphyria because they have
http://bnf.vhn.net/bnf/documents/bnf.1937.html
Florida State University College Of Medicine Digital Library
Disorders. porphyrias Clinical Resources. for. The Merck Manual 17th Ed.1999Table of contents Chapter 14 The porphyrias Table of contents
http://fsumed-dl.slis.ua.edu/clinical/metabolism/inborn/porphyria.htm

Extractions: Clinical Resources by Topic: Metabolic Disorders Porphyrias Clinical Resources Emergency Pediatrics Atlases Radiology ... Miscellaneous Resources See also: Acute Intermittent Porphyria: Access document Porphyria Cutanea Tarda: Access document Hereditary Coproporphyria: Access document Variegate Porphyria: Access document The Erythropoietic Porphyrias: Access document Congenital Erythropoietic Porphyria: Access document Erythropoietic Protoporphyria: Access document Hoffman: Hematology: Basic Principles and Practice 3rd Ed.-2000 (MD Consult):
Florida State University College Of Medicine Digital Library
Disorders. porphyrias Patient/Family Resources. document. Miscellaneousporphyrias Patient/Family Resources Healthfinder (US DHHS) Homepage
http://fsumed-dl.slis.ua.edu/patientinfo/metabolism/inborn/porphyria.htm

Extractions: Patient/Family Resources by Topic: Metabolic Disorders Porphyrias Patient/Family Resources Spanish Miscellaneous See also: MEDLINE plus Medical Encyclopedia: Table of contents Merck Manual Home Edition Table of contents Spanish Miscellaneous Porphyrias Patient/Family Resources National Library of Medicine MEDLINE plus Health Topics: Index YAHOO - Health:Diseases and Conditions:Porphyria
Porphyrias
porphyrias. Definition. The porphyrias are specific precursor. Thissituation is the main characteristic of the porphyrias. Owing
http://www.healthatoz.com/healthatoz/Atoz/ency/porphyrias.html

Extractions: Definition The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing nonprotein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes. Excess porphyrins are excreted as waste in the urine and stool. Overproduction and overexcretion of porphyrins causes low, unhealthy levels of heme and certain important enzymes, creating various physical symptoms. Description Biosynthesis of heme is a multistep process that begins with simple molecules and ends with a large, complex heme molecule. Each step of the chemical pathway is directed by its own task-specific protein, called an enzyme. As a heme precursor molecule moves through each step, an enzyme modifies the precursor in some way. If a precursor molecule is not modified, it cannot proceed to the next step, causing a buildup of that specific precursor. This situation is the main characteristic of the porphyrias. Owing to a defect in one of the enzymes of the heme biosynthesis pathway, protoporphyrins or porphyrins (heme precursors) are prevented from proceeding further along the pathway. These precursors accumulate at the stage of the enzyme defect causing an array of physical symptoms in an affected person. Specific symptoms depend on the point at which heme biosynthesis is blocked and which precursors accumulate. In general, the porphyrias primarily affect the skin and the nervous system. Symptoms can be debilitating or life threatening in some cases. Porphyria is most commonly an inherited condition. It can also, however, be acquired after exposure to poisonous substances.
Porphyrias At The Charles University, Prague, Czech Republic
Welcome to the Experimental porphyrias at the Institute of Pathophysiologyin Prague! Or have you perhaps never heard about porphyrias?
http://www.lf1.cuni.cz/~jkri/porphyria.html

Extractions: This page provides information on our porphyria-related research to any welcome quest. Porphyria research is a traditional topics at the Institute of Pathophysiology of the First Medical Faculty in Prague, Czech Republic. Please note - we are not the only porphyria - oriented department at the University! First Department of Internal Medicine, headed by Professor Kordac, has done a great, great amount of work. Well, during the communist past, of course... And, undoubtedly, the greatest Czech-born porphyria expert living today is Professor Pavel Martasek, recently back from the B.S.Masters group in Texas - but you sure know him as the Hamburg Porphyrias 1997 organiser. For any comments, please write to Jan Krijt at jkri@lf1.cuni.cz. Or have you perhaps never heard about porphyrias?
Porphyrias At The Charles University, Prague, Czech Republic
The Acute Porphyria Theories. From pathophysiological point of view, theacute porphyrias are perhaps more puzzling than nonacute porphyrias.
http://www.lf1.cuni.cz/~jkri/acute.html

Extractions: From pathophysiological point of view, the acute porphyrias are perhaps more puzzling than nonacute porphyrias. A major clinical complication of an acute attack of porphyria is severe peripheral neuropathy. According to current concepts, the pathophysiology of porphyric attack could be related to: - limited availability of heme in the CNS - limited heme saturation of tryptophan pyrrolase - toxic effects of porphyrins and/or porphyrin precursors on CNS and/or peripheral nerves - limited availability of heme as a cofactor of nitric oxide synthase (nNOS and eNOS) In the course of porphyria research, many experimental porphyrias have been developed, including PBG-DE deficient mice and ferrochelatase deficient mice. At this Institute, we are still using old fashioned in vivo models - animals treated with an inhibitor of heme biosynthesis. It is felt that these models could - in spite of their simple design - still throw some light on the pathophysiology of porphyria. Next, we will present some results obtained in mice treated with a competitive inhibitor of protoporphyrinogen oxidase , which form a basis for our porphyria pathophysiology theory.
Porphyrias
porphyrias Compiled by Professor Michael Moore. porphyrias http//medic.bgu.ac.ilA brief look at the two major types, the symptoms and an example is given.
http://www.medlina.com/porphyrias.htm
American Porphyria Foundation - The Porphyrias
The porphyrias. The information that was on this page is now out ofdate. If you have copies of old versions of this page then please
http://www.enterprise.net/apf/overview.html

Extractions: The information that was on this page is now out of date. If you have copies of old versions of this page then please delete those copies because the information no longer reflects the latest research. If you have links to this page then please remove those links because this page is no longer being maintained. For more general information on Porphyria, please see the main page of the American Porphyria Foundation
NorDx: Test Catalog
Special Instructions. Porphyrinogens, Porphyrins, and porphyrias.The porphyrias are emotionally distressful and potentially lethal
http://nordx.mmc.org/testcat/procedure.asp?ProcedureID=30
NSW PORPHYRIN REFERENCE LABORATORY
porphyrias CLINICAL BACKGROUND. The porphyrias are a group of disordersin the haem biosynthetic pathway. They may be the result
http://www.cs.nsw.gov.au/csls/RPAH/porphyria/backgroundporphyrias.htm

Extractions: HOME PAGE PORPHYRIN ... LINKS PORPHYRIAS - CLINICAL BACKGROUND The porphyrias are a group of disorders in the haem biosynthetic pathway. They may be the result of inborn errors of metabolism or else due to toxins in the environment. The diagram and porphyria classification shows the haem pathway and lists the types of porphyria, the symptoms expressed, the mode of inheritance and whether the primary lesion is in the liver or in the erythropoietic system. The primary lesion in each porphyria is a reduction rather than a complete absence in one of the enzymes in the pathway. Normally the pathway can cope because of the presence of at least half of the normal enzyme activity. However, under certain conditions, the pathway becomes activated giving rise to a build up of metabolites at the particular enzyme that is deficient. The activity of ALA synthetase however, varies widely because it is the rate controlling enzyme of the pathway. Being an allosteric enzyme, its activity is feedback inhibited by the end-product haem. Moreover, haem can feedback repress the synthesis of ALA synthetase. An acute attack of neurological porphyria may occur if certain drugs are administered to the patient. This acute attack may include abdominal pain, nausea, vomiting, constipation, neuropathies (peripheral and motor) and psychiatric symptoms. Lists of safe and unsafe drugs in patients with acute porphyria are included on pages 11 and 12.
Porphyrias
porphyrias. 1. CLASSIFICATION. The porphyrias are a heterogeneous groupof either inherited or acquired disorders of haem biosynthesis.
http://ruby.med.cuhk.edu.hk/~cpy/lecture/porphyrias.html

Extractions: 1. CLASSIFICATION The Porphyrias are a heterogeneous group of either inherited or acquired disorders of haem biosynthesis. In these diseases, specific abnormalities of enzymes in the biosynthetic pathway cause generalised clinical abnormalities. They are classified, as shown below, into acute and non-acute porphyria.

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